A SINGLE CASE STUDY ON HALLERVORDEN-SPATZ DISEASE W.S.R. KAMPAVATA – AN INTERVENTIONAL CLINICAL STUDY

Abstract

Pantothenate kinase - associated neurodegeneration (PKAN) , formerly called Hallervorden – Spatz Disease (HSD) , is a rare disorder , usually begins in childhood and is characterized by progressive dystonia , rigidity , tremor , and choreoathetosis . Extensor plantar reponses , dysarthria , and intellectual deterioration become evident during adolescense .Based on symptoms this disease is correlated to Kampavata in ayurveda . Acharya Basavarajiyam has given a clear description by explaining the clinical pictures as karapadatala kampa ( tremor, dystonia , choreoathetosis), deha bhramana ( postural instability ) , matiksheena ( dementia ) and nidrabhanga ( disturbed sleep). A case report of 28 year old male presented with kampa (tremor, cervical dystonia , choreoathetosis), intellectual deterioration, stambha(spasticity in both upper and lower limb),gamanekashtatha(difficulty in walking and sitting without support ) , vakkruchrata(dysarthria), drooling of saliva and was treated in lines of ayurveda in 2 sittings for a period of 20 days each with a gap of one month and the results were encouraging .